Atypical gullian barrie syndrome with bulbar dysfunction and descending paralysis

Atypical gullian barrie syndrome

Abstract

Gullian barrie syndrome (GBS) is a common cause of acute flaccid usually ascending paralysis, characterized by symmetrical weakness of the limbs, and hyporeflexia or areflexia, which reaches a maximum severity within 4 weeks. The motor and sensory axons of the peripheral nerves and the autonomic nervous system may be locally or regionally involved in the atypical presentation group of Guillain-Barré syndrome. We describe the case of a male patient, age 17, who came to our ED with symptoms of bulbar dysfunction and descending arreflexic quadriparesis. A nerve conduction test confirmed the diagnosis of atypical GBS. He was treated for this in the emergency room using mechanical ventilation support and other fundamental supportive care. He was then admitted to the intensive care unit (ICU) and treated for complications that arose during his stay there. After a three-month stay in the ICU, he was moved to the medical ward, where he was discharged with a stable condition and instructions on how to comply with ongoing medical management of his dysautonomia and follow-up.
Key words: Gullian barrie syndrome; atpical Gullian barrie syndrome; bulbar dysfunction;GBS variants; descending weakness